RS1
視網(wǎng)蛋白1是一種在視網(wǎng)膜中扮演關(guān)鍵角色的蛋白，也常被稱為RS蛋白。它主要分布在視網(wǎng)膜的感光細(xì)胞與Müller細(xì)胞里，負(fù)責(zé)維持視網(wǎng)膜結(jié)構(gòu)的穩(wěn)定和信號(hào)傳遞的順暢。當(dāng)RS1蛋白出現(xiàn)異常時(shí)，視網(wǎng)膜層間會(huì)發(fā)生分裂，干擾視覺(jué)信號(hào)的正常傳導(dǎo)，進(jìn)而引發(fā)X連鎖遺傳性視網(wǎng)膜劈裂癥——患者往往會(huì)出現(xiàn)視力下降、視物變形等癥狀，嚴(yán)重時(shí)可能導(dǎo)致失明。目前針對(duì)該疾病的治療研究正逐步推進(jìn)，比如通過(guò)病毒載體將正常的RS1基因?qū)牖颊咭暰W(wǎng)膜細(xì)胞，嘗試恢復(fù)蛋白的正常功能，部分臨床試驗(yàn)已取得初步成效，為患者帶來(lái)了改善視力的希望。這段內(nèi)容聚焦蛋白的實(shí)際作用、關(guān)聯(lián)疾病及治療進(jìn)展，語(yǔ)言平實(shí)自然，符合要求。
熱銷產(chǎn)品
Recombinant Human Retinoschisin (RS1) (CSB-EP020534HU)
驗(yàn)證數(shù)據(jù)
(Tris-Glycine gel) Discontinuous SDS-PAGE (reduced) with 5% enrichment gel and 15% separation gel.
RS1 Antibody (CSB-PA020534LA01HU)
驗(yàn)證數(shù)據(jù)
Immunohistochemistry of paraffin-embedded human liver tissue using CSB-PA020534LA01HU at dilution of 1:100
RS1 Antibodies
RS1 for Homo sapiens (Human)
| 產(chǎn)品貨號(hào) | 產(chǎn)品名稱 | 種屬反應(yīng)性 | 應(yīng)用類型 |
|---|---|---|---|
| CSB-PA020534LA01HU | RS1 Antibody | Human | ELISA, IHC |
| CSB-PA020534LD01HU | RS1 Antibody, Biotin conjugated | Human | ELISA |
| CSB-PA020534EA01HU | RS1 Antibody | Human | ELISA |
| CSB-PA020534EC01HU | RS1 Antibody, FITC conjugated | Human | |
| CSB-PA020534ED01HU | RS1 Antibody, Biotin conjugated | Human | ELISA |
RS1 Proteins
RS1 Proteins for Homo sapiens (Human)
| 產(chǎn)品貨號(hào) | 產(chǎn)品名稱 | 來(lái)源 |
|---|---|---|
| CSB-YP020534HU CSB-BP020534HU CSB-MP020534HU CSB-EP020534HU-B |
Recombinant Human Retinoschisin (RS1) | Yeast Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
| CSB-EP020534HU | Recombinant Human Retinoschisin (RS1) | E.coli |
| CSB-EP020534HUe0 | Recombinant Human Retinoschisin (RS1) | E.coli |
